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Case Reports
Open AccessOral-facial-digital syndrome, Type I: A case report
Oral-facial-digital syndrome, Type I: A case report
1Paediatric Dentistry and Orthodontics, Faculty of Dentistry, The University of Hong Kong, Prince Philip Dental Hospital, 34 Hospital Road, Hong Kong SAR
DOI: 10.17796/jcpd.26.2.d34417040174j35x Vol.26,Issue 2,April 2002 pp.211-215
Published: 01 April 2002
*Corresponding Author(s): N.M. King E-mail: nmking@glink.net.hk
Abstract
Oral-facial-digital syndrome is a group of congenital anomalies, which affects the face, oral structures and digits. There are nine subtypes. OFDS type I, is x-linked dominant trait mostly affecting females. Reports of OFDS type 1 in Asians are extremely rare. This paper shows a case of OFDS type I, in a southern Chinese girl, who in addition to most of the classic features, had fusion of the mandibular canine and lateral incisor teeth.
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N.M. King,A.M.E. Sanares. Oral-facial-digital syndrome, Type I: A case report. Journal of Clinical Pediatric Dentistry. 2002. 26(2);211-215.
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