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Clinical treatment of oral manifestations of Beckwith-Wiedeman syndrome in a child

  • Aldo Giancotti1,*,
  • Gaia Romanini1
  • Raffaella Docimo1
  • Claudio Arcuri1

1Department of Orthodontics, Univeristy of Rome "Tor Vergata", Ospedale Fatebenefratelli, Isola Tiberina

DOI: 10.17796/jcpd.27.4.6356k0231w213386 Vol.27,Issue 4,October 2003 pp.377-380

Published: 01 October 2003

*Corresponding Author(s): Aldo Giancotti E-mail: giancott@uniroma2.it

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Abstract

Orthodontic treatment in a young patient with Beckwith-Wiedeman Syndrome (BWS) is reported and a multidisciplinary approach to the management of this syndrome is reviewed. The patient presented with a tendency to Class III malocclusion, an open-bite and a slight macroglossia, which was treated at an early age by glossotomy. It was decided to monitor growth without treatment and to wait for the best time to begin therapy. It was based only on functional rehabilitation, without any fixed appliances, in which optimum intercuspation of the teeth and the skeletal Class I relationship was achieved and maintained after the retention period of three years. In conclusion the treatment of BWS patients requires a multidisciplinary approach that includes orthodontics, orthopaedics and surgical interven-tion. It is also necessary to underline the significance of diagnosis at an early age and timely treatment to reduce the development of dento-skeletal alterations.

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Aldo Giancotti,Gaia Romanini,Raffaella Docimo,Claudio Arcuri. Clinical treatment of oral manifestations of Beckwith-Wiedeman syndrome in a child. Journal of Clinical Pediatric Dentistry. 2003. 27(4);377-380.

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https://www.jocpd.com/articles/10.17796/jcpd.27.4.6356k0231w213386

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