Article Data

  • Views 1039
  • Dowloads 138

Original Research

Open Access

Atypical Hallerman-Streif Syndrome: A Case Report

  • Manju Gopakumar1
  • Amitha M Hedge1,*,

1Department of Pedodontics and Preventive Dentistry, A.B. Shetty Memorial Institute of Dental Dental Sciences

DOI: 10.17796/jcpd.30.1.91036513g7u55705 Vol.30,Issue 1,January 2006 pp.73-76

Published: 01 January 2006

*Corresponding Author(s): Amitha M Hedge E-mail: amipedo@yahoo.co.in

Abstract

Hallerman Streif syndrome is a rare congenital disorder characterized by dyscephaly, dental anom-alies, proportionate nazism ,hypotrichosis, cutaneous atrophy limited to the head ,bilateral congenital cataracts and bilateral microphthalmia .Despite the marked craniofacial characteristics and oral find-ings,a relative lack of reports in the dental literature has been noted. In this article, a case of a 8 year old boy with dental problems is described.

Cite and Share

Manju Gopakumar,Amitha M Hedge. Atypical Hallerman-Streif Syndrome: A Case Report. Journal of Clinical Pediatric Dentistry. 2006. 30(1);73-76.

References

1. Aubry, M.variété singuliere d’alopécie congénitale: alopécie suturale. Ann dermatol syphilige (paris) 4:899–900,1893.

2. Hallermalm W. Vogelgesicht und cataracta congenita klin monatsbl Augenheilkd 113:315–318, 1984.

3. Strei EB. Dysmorphie mandibulo-faciale (tête d’oiseau) et altération oculaires opthalmologica 120:79–83, 1950.

4. Spoerl G, Romano P. Penetrating Keratoplasty In a complicated mandibulofacial dyscephaly. J Pediatr Ophthalmol 10:61–64, 1973.

5. Koliopoulos J, Palimeris G. Atypical Hallermann-Streif François Syndrome In Three Successive Generations. J Pediatr Ophthalmol 12:235–239, 1975.

6. François MJ. A new syndrome: Dyscephalia with bird face and dental anomalies, nanism, hypotrichosis. utaneodus atrophy, microphthalmia and congenital cataract. Arch ophtal mol 60:842–862, 1958.

7. Cohen MM. Hallermann-Streif Syndrome: A Review. Am J Med Genet 41:488:499, 1991.

8. Sclaroff A, Eppley Bl. Evaluation and surgical correction of the facial skeletal deformity in Hallermann Streif Syndrome. Int J Oral Maxillofac Surg 16:738–744, 1987.

9. Kurlander GJ,Lavy NW, Campbell JA. Roentgen differentiation of the oculodentodigital syndrome and the Hallermann Streif Syndrome In infancy. Radiology 86:77–85, 1966.

10. Christian CL, Lachman RS, Aylsworth AS, Fujimoto A. Gorlin RJ, Lipson MH,Graham JM. Radiological findings in Hallermann Streif syndrome: Report of five cases and a review of literature. Am J Med Genet 41:508–514,1991.

11. Suzuki Y, Fujii T, Fukuyama Y. Hallermann - Streif Syndrome Dev Med Child Neurol 12:496–506, 1970.

12. Hopkins DJ, Horan EC. Glaucoma in the Hallermann Streif Syndrome. BrJ Ophthalmol 54:416–422, 1970.

13. Sugar A. BiggerJf. Podos SM.Hallermann-Sterif-François Syndrome. J Pediatr Ophthalmol 8:234–238, 1970.

14. Steele RW, Bass JW, Hallenmann – Streif Syndrome: Clinical and prognostic considerations. Am J Dis Child 120:462–465, 1970.

15. Srivastava S, Mandibulo-oculo-facial dyscephaly. Br J Ophthalmol 58:543–549, 1966. 16. Sharp EC,Kopel HM Craniofacial and oral manifestation oculomandibulodyscephaly (Hallermann–Streif Syndrome) Surg: 30:488–497, 1970.

17. Ohishi M, Murakami E, Haita T, Naruse T. Sugino M, Inoma H, Hallermann-Streif Syndrome and its oral implications. J Dent Child 40:32–37, 1986.

Abstracted / indexed in

Science Citation Index Expanded (SciSearch) Created as SCI in 1964, Science Citation Index Expanded now indexes over 9,500 of the world’s most impactful journals across 178 scientific disciplines. More than 53 million records and 1.18 billion cited references date back from 1900 to present.

Biological Abstracts Easily discover critical journal coverage of the life sciences with Biological Abstracts, produced by the Web of Science Group, with topics ranging from botany to microbiology to pharmacology. Including BIOSIS indexing and MeSH terms, specialized indexing in Biological Abstracts helps you to discover more accurate, context-sensitive results.

Google Scholar Google Scholar is a freely accessible web search engine that indexes the full text or metadata of scholarly literature across an array of publishing formats and disciplines.

JournalSeek Genamics JournalSeek is the largest completely categorized database of freely available journal information available on the internet. The database presently contains 39226 titles. Journal information includes the description (aims and scope), journal abbreviation, journal homepage link, subject category and ISSN.

Current Contents - Clinical Medicine Current Contents - Clinical Medicine provides easy access to complete tables of contents, abstracts, bibliographic information and all other significant items in recently published issues from over 1,000 leading journals in clinical medicine.

BIOSIS Previews BIOSIS Previews is an English-language, bibliographic database service, with abstracts and citation indexing. It is part of Clarivate Analytics Web of Science suite. BIOSIS Previews indexes data from 1926 to the present.

Journal Citation Reports/Science Edition Journal Citation Reports/Science Edition aims to evaluate a journal’s value from multiple perspectives including the journal impact factor, descriptive data about a journal’s open access content as well as contributing authors, and provide readers a transparent and publisher-neutral data & statistics information about the journal.

Scopus: CiteScore 1.8 (2023) Scopus is Elsevier's abstract and citation database launched in 2004. Scopus covers nearly 36,377 titles (22,794 active titles and 13,583 Inactive titles) from approximately 11,678 publishers, of which 34,346 are peer-reviewed journals in top-level subject fields: life sciences, social sciences, physical sciences and health sciences.

Submission Turnaround Time

Conferences

Top