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Original Research

Open Access

Ectodermal dysplasia—an unusual dental presentation

  • F S Ryan1
  • C Mason2,*,
  • J I Harper3

1Senior House Officer Paediatric Dentistry, Dental and Maxillofacial Department, Great Ormond Street Hospital for Children

2Consultant Paediatric Dentistry, Dental and Maxillofacial Department, Great Ormond Street Hospital for Children

3Department of Dermatology, Great Ormond Street Hospital for Children

DOI: 10.17796/jcpd.30.1.x603wm13gh6k6316 Vol.30,Issue 1,January 2006 pp.55-58

Published: 01 January 2006

*Corresponding Author(s): C Mason E-mail: masonc1@gosh.nhs.uk

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Abstract

Ectodermal dysplasia (ED) is a rare group of disorders affecting the hair, teeth, nails and sweat glands to a variable degree. There is a wide range of clinical presentation of ED. Missing teeth or abnormal tooth form may be the first indicator of the presence of the disorder. There is typically hypodontia with microdontia. We present an unusual case of ED with severe hypodontia and macrodontia affecting all first permanent molar teeth. We also consider the classification and presentation of this disorder.


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F S Ryan,C Mason,J I Harper. Ectodermal dysplasia—an unusual dental presentation. Journal of Clinical Pediatric Dentistry. 2006. 30(1);55-58.

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https://www.jocpd.com/articles/10.17796/jcpd.30.1.x603wm13gh6k6316

References

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