Multiple developmental dental anomalies and hypermobility type Ehlers-Danlos syndrome

Concurrent existence of multiple developmental dental anomalies: hypodontia of permanent mandibular incisors, dentin dysplasia, transmigration, root dilaceration, ectopic eruption and delayed eruption combined with systemic abnormal-ities including joint hyperlaxity and skin hyperextensibility aided in diagnosis of a sporadic case of hypermobility type of Ehlers-Danlos syndrome in a Jordanian Arab male. In dental practice the presence of multiple developmental den-tal anomalies expressing simultaneous defects in different stages of tooth development should raise suspicion of possi-ble of manifestation of an underlying systemic abnormality.

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